These Arnold Chiari Malformations Type 1 abbreviated as ACM are the structural defects of cerebellum and brain stem. It exhibits the downward displacement of the cerebellum at the base of the skull through the foramen magnum. Syringomyelia is the chronic degeneration and cyst formation on the spinal cord usually extended upto the Medulla Oblongata and Pons. Many of time it is associated with Ac malformations. 1 Women are three times more likely to have this congenital defect. Diagnosis of Arnold Chiari Malformation Type 1 is mainly based on clinical suspicion. Definite diagnosis requires assessment of patient’s detailed history, neurological examination and medical imaging. 1,2 In this article we report a case of Arnold Chiari malformations Type 1 (ACM) with Syringomyelia in an 18 year old male patient.
