A rare case of cystic lesions of jaw (odontogenic keratocystic lesions) - gorlin goltz syndrome

Gorlin-Goltz syndrome is a rare autosomal dominant inherited disorder identified by the presence  of multiple odontogenic keratocysts, alongside a range of cutaneous, dental, osseous, ophthalmic, genital and neurological abnormalities. Prompt diagnosis is crucial as it can advance to aggressive basal cell carcinomas and neoplasias. Instances of Gorlin-Goltz syndrome in India are rare. Timely diagnosis and intervention play a critical role in mitigating the severity of long-term complications associated with this syndrome.(1)