Unrevealingthe Mysteries Of Cherubism- A Case Report With Brief Review

Review Article
Biju Baby Joseph and Shiny George
DOI: 
http://dx.doi.org/10.24327/ijrsr.2017.0804.0206
Subject: 
Medicine
KeyWords: 
-
Abstract: 

Background: Cherubism is a benign fibro-osseous lesion involving jaw bones predominantly mandible. It appears to be a hereditary disease with an autosomal dominant pattern of inheritance. The lesion starts in childhood gradual in onset involving both sides causing asymmetry of facial profile. It regress spontaneously at the onset of puberty. Aim: Reveling the unrevealed about cherubism: a fibro-osseous lesion affecting manly jaw bones. Case: we report a case of cherubism seen in the post pubertal age. We report a case for which panoramic and occlusal radiographs were taken, which are sufficient for diagnosis of this case. Clinical and radiological findings were discussed. Conclusion: A rare disease but affected individuals have a significant impact on the health and general wellbeing. Affected bone is predominantly mandible causing facial asymmetry. Genetic test are used to diagnose the case .Surgical intervention, orthodontic treatment along with cosmetic /plastic surgery are a common line of management. At the higher end genetic therapy can also be regarded. To conclude we report a case of cherubism seen in a postpuberal individual with classic clinical features, sequence of progression, and radiographic features suttle to the diseases.