Renal cell carcinoma also known as (Hypernephroma, Grawitz tumor, Renal adenocarcinoma) is a kidney cancer that originates in the lining of the proximal convoluted tubule. Adult clear cell carcinoma with extensive rhabdoid features is a rare clinical entity. Rhabdoid morphology in renal cell carcinoma resembling malignant rhabdoid tumor of kidney was first described in 1991, but this phenomenon should be strictly distinguished from extrarenal malignant rhabdoid tumors because the prognosis and therapeutic strategies differ significantly. Rhabdoid features have been recently identified as a morphological variant of renal cell carcinoma associated with poor prognosis and a marker of high risk for metastasis. Rhabdoid cells are characterized by a large abundant eosinophilic cytoplasm with an irregular eccentric nucleus and a rounded eosinophilic cytoplasmic inclusion. A 45 years old male came with a history of pain in left lumbar and epigastric region since 4-5 months.
